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Valvular Disease*

Valvular Disease*: Excerpt from A Pocket Manual of Differential Diagnosis

Aortic Valve


Stenosis
   Valvular
       Congenital
       Rheumatic
       Calcific (senile)
       Atherosclerotic
       Rheumatoid
       Ochronosis
   Supravalvular
   Subvalvular
Regurgitation
   Congenital
       Bicuspid aortic valve
          Isolated
          Associated with
              Coarctation
              Ventricular septal defect
              Patent ductus arteriosus
       Tricuspid aortic valve
          Isolated
          Associated with
              Ventricular septal defect
              Valvular aortic stenosis
              Supravalvular aortic stenosis
              Subvalvular aortic stenosis
              Congenital aneurysm of sinus of Valsalva
              Cusp fenestrations
       Quadricuspid aortic valve
   Acquired
       Valvular
          Rheumatic heart disease
          Bacterial endocarditis
          Calcific aortic valve disease
          Atherosclerosis
          Traumatic valve rupture
          Dissection of the aorta
          Post–aortic valve surgery
              Postvalvulotomy
              Leakage around prosthesis
              Endocarditis
          Miscellaneous
              Ankylosing spondylitis
              Reiter's syndrome
              Rheumatoid arthritis
              Whipple's disease
              Crohn's disease
              Jaccoud's arthropathy
              Systemic lupus erythematosus
              Scleroderma
              Myxomatous degeneration
              Pseudoxanthoma elasticum
              Mucopolysaccharidoses
              Osteogenesis imperfecta
              Cusp fenestrations
              Methysergide
       Aortic dilatation or distortion
          Senile dilatation
          Cystic medial necrosis with or without Marfan's
syndrome
          Takayasu's disease
          Relapsing polychondritis
          Syphilis
          Ankylosing spondylitis
          Psoriatic arthritis
          Ulcerative colitis with arthritis
          Reiter's syndrome
          Giant cell arteritis
          Ehlers-Danlos syndrome
          Hypertension
          Cogan's syndrome
          Behçet's syndrome

Mitral Valve


Stenosis
   Congenital
   Rheumatic
   Carcinoid syndrome
   Marantic endocarditis
   Systemic lupus erythematosus
   Calcific
   Lutembacher's syndrome
   Amyloidosis
   Rheumatoid arthritis
   Hunter-Hurler disease
   Methysergide
Regurgitation
   Congenital
       Isolated mitral regurgitation
       Hypertrophic cardiomyopathy
       Connective tissue disorders
          Ehlers-Danlos syndrome
          Hurler's syndrome
          Marfan's syndrome
          Pseudoxanthoma elasticum
          Osteogenesis imperfecta
       Atrioventricular cushion defect
       Endocardial fibroelastosis
       Parachute mitral valve complex
       Hypoplastic left heart syndrome
       Anomalous left coronary artery from pulmonary artery
       Congenital mitral stenosis
       Corrected transposition of great vessels with or without Ebstein's malformation
       Supravalvular ring of left atrium
   Acquired
       Coronary heart disease
       Rheumatic (acute or chronic)
       Mitral valve prolapse syndrome
       Papillary muscle dysfunction
          Coronary heart disease with or without myocardial infarction
          Neoplasm
          Myocardial abscess
          Granulomas
          Sarcoidosis
          Amyloidosis
       Ruptured or abnormal chordae tendineae (e.g., idiopathic myxomatous proliferation)
       Bacterial endocarditis
       Calcified mitral annulus
          Idiopathic systemic hypertension
          Aortic stenosis
          Diabetes
          Chronic renal failure with secondary hyperparathyroidism
       Left ventricular dilatation or aneurysm (e.g., dilated cardiomyopathy)
       Aortic valve disease
       Prosthetic valve disruption
       Trauma
       Post–cardiac surgery
       Rheumatoid arthritis
       Ankylosing spondylitis
       Scleroderma
       Systemic lupus erythematosus
       Left atrial myxoma
       Spontaneous rupture
       Carcinoid syndrome
       Giant left atrium
       Kawasaki disease
       Hypereosinophilic syndrome

Pulmonic Valve


Stenosis
   Congenital
       Valvular stenosis
       Valvular dysplasia (e.g., Noonan's syndrome)
       Tetralogy of Fallot
       Supravalvular aortic stenosis syndrome
   Acquired
       Intrinsic valvular lesions
          Rheumatic disease
          Carcinoid syndrome
          Endocarditis
          Primary neoplasm
       Extrinsic lesions
          Neoplasm
          Aortic or septal aneurysm
          Sinus of Valsalva aneurysm
          Constrictive pericarditis
   Regurgitation
   Congenital
       Absent pulmonic valve
       Isolated pulmonic regurgitation
       Associated with:
          Tetralogy of Fallot
          Ventricular septal defect
          Pulmonic valvular stenosis
          Idiopathic dilatation of pulmonic valve
   Acquired
       Valve ring dilatation secondary to pulmonary hypertension of any cause (see 2-G, Right Heart Failure)
       Pulmonary artery dilatation, idiopathic
       Bacterial endocarditis
       Post–pulmonic valve surgery
       Rheumatic disease
       Trauma
       Syphilis
       Carcinoid syndrome
       Marfan's syndrome
       Induced by pulmonary artery catheter

Tricuspid Valve


Stenosis
   Rheumatic heart disease (acute and chronic)
   Carcinoid syndrome
   Fibroelastosis
   Tricuspid atresia
   Endomyocardial fibrosis
Regurgitation
   Right ventricular dilatation of any cause (e.g., mitral stenosis)
   Pulmonary hypertension (see 2-G, Right Heart Failure)
   Rheumatic heart disease
   Right ventricular papillary muscle dysfunction
   Myxomatous valve and chordae (usually in association with mitral valve prolapse with or without atrial septal defect)
   Trauma
   Bacterial endocarditis
   Carcinoid syndrome
   Ebstein's anomaly
   Common atrioventricular canal
   Ventricular septal aneurysm
   Right atrial myxoma
   Constrictive pericarditis
   Endomyocardial fibrosis
   Methysergide
   Systemic lupus erythematosus
   Radiation injury
   Thyrotoxicosis
   Isolated lesion
   After surgical excision
   Marfan's syndrome
   Rheumatoid arthritis

References

1. Braunwald E: Valvular Heart Disease, p. 1007. See Bibliography, 1.

2. Weiss JL: Valvular Heart Disease, p. 435. See Bibliography, 5.

*See also 2-F.

Book Source Details

  • Book Title: A Pocket Manual of Differential Diagnosis
  • Author(s): Stephen N. Adler, Dianne B. Gasbarra
  • Year of Publication: 1999
  • Copyright Details: A Pocket Manual of Differential Diagnosis, Copyright © 1999 Lippincott Williams & Wilkins.

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Copyright notice for book excerpts: Copyright © 2008 Lippincott Williams & Wilkins. All rights reserved.




More About This Book:
Title: A Pocket Manual of Differential Diagnosis
Authors: Stephen N. Adler, Dianne B. Gasbarra
Publisher: Lippincott Williams & Wilkins
Copyright: 1999
ISBN: 0-78171-943-7

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