1 per 250 - 500 people from Hmong populations in southeast Asia and America suffer from 2-methylbutyryl-coenzyme A dehydrogenase deficiency though many are asymptomatic, Genetics Home Reference website
| Country/Region | Extrapolated Prevalence | Population Estimated Used |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in North America (Extrapolated Statistics) |
| USA | 1,174,621 | 293,655,4051 |
| Canada | 130,031 WARNING! (Details) | 32,507,8742 |
| Mexico | 419,838 WARNING! (Details) | 104,959,5942 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in Central America (Extrapolated Statistics) |
| Belize | 1,091 WARNING! (Details) | 272,9452 |
| Guatemala | 57,122 WARNING! (Details) | 14,280,5962 |
| Nicaragua | 21,439 WARNING! (Details) | 5,359,7592 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in Caribbean (Extrapolated Statistics) |
| Puerto Rico | 15,591 WARNING! (Details) | 3,897,9602 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in South America (Extrapolated Statistics) |
| Brazil | 736,404 WARNING! (Details) | 184,101,1092 |
| Chile | 63,295 WARNING! (Details) | 15,823,9572 |
| Colombia | 169,243 WARNING! (Details) | 42,310,7752 |
| Paraguay | 24,765 WARNING! (Details) | 6,191,3682 |
| Peru | 110,177 WARNING! (Details) | 27,544,3052 |
| Venezuela | 100,069 WARNING! (Details) | 25,017,3872 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in Northern Europe (Extrapolated Statistics) |
| Denmark | 21,653 WARNING! (Details) | 5,413,3922 |
| Finland | 20,858 WARNING! (Details) | 5,214,5122 |
| Iceland | 1,175 WARNING! (Details) | 293,9662 |
| Sweden | 35,945 WARNING! (Details) | 8,986,4002 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in Western Europe (Extrapolated Statistics) |
| Britain (United Kingdom) | 241,082 WARNING! (Details) | 60,270,708 for UK2 |
| Belgium | 41,393 WARNING! (Details) | 10,348,2762 |
| France | 241,696 WARNING! (Details) | 60,424,2132 |
| Ireland | 15,878 WARNING! (Details) | 3,969,5582 |
| Luxembourg | 1,850 WARNING! (Details) | 462,6902 |
| Monaco | 129 WARNING! (Details) | 32,2702 |
| Netherlands (Holland) | 65,272 WARNING! (Details) | 16,318,1992 |
| United Kingdom | 241,082 WARNING! (Details) | 60,270,7082 |
| Wales | 11,672 WARNING! (Details) | 2,918,0002 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in Central Europe (Extrapolated Statistics) |
| Austria | 32,699 WARNING! (Details) | 8,174,7622 |
| Czech Republic | 4,984 WARNING! (Details) | 1,0246,1782 |
| Germany | 329,698 WARNING! (Details) | 82,424,6092 |
| Hungary | 40,129 WARNING! (Details) | 10,032,3752 |
| Liechtenstein | 133 WARNING! (Details) | 33,4362 |
| Poland | 154,505 WARNING! (Details) | 38,626,3492 |
| Slovakia | 21,694 WARNING! (Details) | 5,423,5672 |
| Slovenia | 8,045 WARNING! (Details) | 2,011,473 2 |
| Switzerland | 29,803 WARNING! (Details) | 7,450,8672 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in Eastern Europe (Extrapolated Statistics) |
| Belarus | 41,242 WARNING! (Details) | 10,310,5202 |
| Estonia | 5,366 WARNING! (Details) | 1,341,6642 |
| Latvia | 9,225 WARNING! (Details) | 2,306,3062 |
| Lithuania | 14,431 WARNING! (Details) | 3,607,8992 |
| Russia | 575,896 WARNING! (Details) | 143,974,0592 |
| Ukraine | 190,928 WARNING! (Details) | 47,732,0792 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in the Southwestern Europe (Extrapolated Statistics) |
| Azerbaijan | 31,473 WARNING! (Details) | 7,868,3852 |
| Georgia | 18,775 WARNING! (Details) | 4,693,8922 |
| Portugal | 42,096 WARNING! (Details) | 10,524,1452 |
| Spain | 161,123 WARNING! (Details) | 40,280,7802 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in Southern Europe (Extrapolated Statistics) |
| Greece | 42,590 WARNING! (Details) | 10,647,5292 |
| Italy | 232,229 WARNING! (Details) | 58,057,4772 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in the Southeastern Europe (Extrapolated Statistics) |
| Albania | 14,179 WARNING! (Details) | 3,544,8082 |
| Bosnia and Herzegovina | 1,630 WARNING! (Details) | 407,6082 |
| Bulgaria | 30,071 WARNING! (Details) | 7,517,9732 |
| Croatia | 17,987 WARNING! (Details) | 4,496,8692 |
| Macedonia | 8,160 WARNING! (Details) | 2,040,0852 |
| Romania | 89,422 WARNING! (Details) | 22,355,5512 |
| Serbia and Montenegro | 43,303 WARNING! (Details) | 10,825,9002 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in Northern Asia (Extrapolated Statistics) |
| Mongolia | 11,005 WARNING! (Details) | 2,751,3142 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in Central Asia (Extrapolated Statistics) |
| Kazakhstan | 60,574 WARNING! (Details) | 15,143,7042 |
| Tajikistan | 28,046 WARNING! (Details) | 7,011,556 2 |
| Uzbekistan | 105,641 WARNING! (Details) | 26,410,4162 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in Eastern Asia (Extrapolated Statistics) |
| China | 5,195,390 WARNING! (Details) | 1,298,847,6242 |
| Hong Kong s.a.r. | 27,420 WARNING! (Details) | 6,855,1252 |
| Japan | 509,332 WARNING! (Details) | 127,333,0022 |
| Macau s.a.r. | 1,781 WARNING! (Details) | 445,2862 |
| North Korea | 90,790 WARNING! (Details) | 22,697,5532 |
| South Korea | 192,935 WARNING! (Details) | 48,233,7602 |
| Taiwan | 90,999 WARNING! (Details) | 22,749,8382 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in Southwestern Asia (Extrapolated Statistics) |
| Turkey | 275,575 WARNING! (Details) | 68,893,9182 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in Southern Asia (Extrapolated Statistics) |
| Afghanistan | 114,054 WARNING! (Details) | 28,513,6772 |
| Bangladesh | 565,361 WARNING! (Details) | 141,340,4762 |
| Bhutan | 8,742 WARNING! (Details) | 2,185,5692 |
| India | 4,260,282 WARNING! (Details) | 1,065,070,6072 |
| Pakistan | 636,785 WARNING! (Details) | 159,196,3362 |
| Sri Lanka | 79,620 WARNING! (Details) | 19,905,1652 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in Southeastern Asia (Extrapolated Statistics) |
| East Timor | 4,077 WARNING! (Details) | 1,019,2522 |
| Indonesia | 953,811 WARNING! (Details) | 238,452,9522 |
| Laos | 24,272 WARNING! (Details) | 6,068,1172 |
| Malaysia | 94,089 WARNING! (Details) | 23,522,4822 |
| Philippines | 344,966 WARNING! (Details) | 86,241,6972 |
| Singapore | 17,415 WARNING! (Details) | 4,353,8932 |
| Thailand | 259,462 WARNING! (Details) | 64,865,5232 |
| Vietnam | 330,651 WARNING! (Details) | 82,662,8002 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in the Middle East (Extrapolated Statistics) |
| Gaza strip | 5,299 WARNING! (Details) | 1,324,9912 |
| Iran | 270,012 WARNING! (Details) | 67,503,2052 |
| Iraq | 101,498 WARNING! (Details) | 25,374,6912 |
| Israel | 24,796 WARNING! (Details) | 6,199,0082 |
| Jordan | 22,444 WARNING! (Details) | 5,611,2022 |
| Kuwait | 9,030 WARNING! (Details) | 2,257,5492 |
| Lebanon | 15,108 WARNING! (Details) | 3,777,2182 |
| Saudi Arabia | 103,183 WARNING! (Details) | 25,795,9382 |
| Syria | 72,067 WARNING! (Details) | 18,016,8742 |
| United Arab Emirates | 10,095 WARNING! (Details) | 2,523,9152 |
| West Bank | 9,244 WARNING! (Details) | 2,311,2042 |
| Yemen | 80,099 WARNING! (Details) | 20,024,8672 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in Northern Africa (Extrapolated Statistics) |
| Egypt | 304,469 WARNING! (Details) | 76,117,4212 |
| Libya | 22,526 WARNING! (Details) | 5,631,5852 |
| Sudan | 156,592 WARNING! (Details) | 39,148,1622 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in Western Africa (Extrapolated Statistics) |
| Congo Brazzaville | 11,992 WARNING! (Details) | 2,998,0402 |
| Ghana | 83,028 WARNING! (Details) | 20,757,0322 |
| Liberia | 13,562 WARNING! (Details) | 3,390,6352 |
| Niger | 45,442 WARNING! (Details) | 11,360,5382 |
| Nigeria | 71,001 WARNING! (Details) | 12,5750,3562 |
| Senegal | 43,408 WARNING! (Details) | 10,852,1472 |
| Sierra leone | 23,535 WARNING! (Details) | 5,883,8892 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in Central Africa (Extrapolated Statistics) |
| Central African Republic | 14,969 WARNING! (Details) | 3,742,4822 |
| Chad | 38,154 WARNING! (Details) | 9,538,5442 |
| Congo kinshasa | 233,268 WARNING! (Details) | 58,317,0302 |
| Rwanda | 32,954 WARNING! (Details) | 8,238,6732 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in Eastern Africa (Extrapolated Statistics) |
| Ethiopia | 285,346 WARNING! (Details) | 71,336,5712 |
| Kenya | 131,928 WARNING! (Details) | 32,982,1092 |
| Somalia | 33,218 WARNING! (Details) | 8,304,6012 |
| Tanzania | 144,283 WARNING! (Details) | 36,070,7992 |
| Uganda | 105,561 WARNING! (Details) | 26,390,2582 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in Southern Africa (Extrapolated Statistics) |
| Angola | 43,914 WARNING! (Details) | 10,978,5522 |
| Botswana | 6,556 WARNING! (Details) | 1,639,2312 |
| South Africa | 177,793 WARNING! (Details) | 44,448,4702 |
| Swaziland | 4,676 WARNING! (Details) | 1,169,2412 |
| Zambia | 44,102 WARNING! (Details) | 11,025,6902 |
| Zimbabwe | 14,687 WARNING! (Details) | 1,2671,8602 |
| 2-methylbutyryl-coenzyme A dehydrogenase deficiency in Oceania (Extrapolated Statistics) |
| Australia | 79,652 WARNING! (Details) | 19,913,1442 |
| New Zealand | 15,975 WARNING! (Details) | 3,993,8172 |
| Papua New Guinea | 21,681 WARNING! (Details) | 5,420,2802 |
The word 'prevalence' of 2-methylbutyryl-coenzyme A dehydrogenase deficiency usually means the estimated population
of people who are managing 2-methylbutyryl-coenzyme A dehydrogenase deficiency at any given time (i.e. people with 2-methylbutyryl-coenzyme A dehydrogenase deficiency).
The term 'incidence' of 2-methylbutyryl-coenzyme A dehydrogenase deficiency means the annual diagnosis rate,
or the number of new cases of 2-methylbutyryl-coenzyme A dehydrogenase deficiency diagnosed each year (i.e. getting 2-methylbutyryl-coenzyme A dehydrogenase deficiency).
Hence, these two statistics types can differ:
a short disease like flu can have high annual incidence but low prevalence,
but a life-long disease like diabetes has a low annual incidence but high prevalence.
For more information see about prevalence and incidence statistics.